A 64-year-old man who was diagnosed with type I neurofibromatosis was referred to our hospital with a pelvic mass incidentally found by ultrasonography. When examined by CT and MRI, the mass in the pelvis was 5 x 3 x 2 cm. In addition, another mass was found close to the obturator nerve at the S1-2 level. Transrectal biopsy was carried out, and a diagnosis of neurofibroma suspicious for low grade malignancy was made. We performed surgical resection of both of the tumors. The resected tumor was pathologically diagnosed as retroperitoneal malignant peripheral nerve sheath tumor (MPNST). We report our case and review the literature of MPNST detected in type I neurofibromatosis.
[Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report] Publishing Authors By Initials
[Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report] Journal Published:
PUBLICATION TYPE: Journal Article
Journal: Hinyokika kiyo. Acta urologica Japonica
VOLUME: 53
Page Numbers: 619-21
Journal Abbreviation:
ISSN: 0018-1994
DAY: 15
MONTH: Sep
YEAR: 2007
[Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report] Information
Number of References:
LANGUAGE: jpn
NlmUniqueID: 421145
[Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report] Keywords Mesh Terms:
KEYWORDS:
MESH TERMS:
Chemical & Substance for Abstract: [Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report] Information
Substance Name:
Registry Number:
Grant and Affiliation Information for [Retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis I: a case report]
AFFILIATION: The Department of Urology, Saiseikai Izuo Hospital.
Country: Japan
AGENCY:
GRANT:
ACRONYM:
MEDLINETA: Hinyokika Kiyo
REFSOURCE:
DATABASENAME:
ACCESSION NUMBER:
Number Hits: 0
Retroperitoneal malignant peripheral nerve sheath tumor MPNST in a patient with neurofibromatosis I: a case report Related Publications