Pentalogy of Cantrell is a rare congenital defect associated with five ventral midline anomalies and high mortality. An obstetric sonogram revealed a fetus with a body wall defect suggesting a diagnosis of this condition. Soon after birth, the infant underwent a closure of the upper abdominal wall defect followed by the successful repair of double-outlet right ventricle and pulmonary valve stenosis at the age of 5 months. The patient is currently alive and well 3.5 years after surgery. It is concluded that a deliberate therapeutic strategy based on the intrauterine diagnosis may alter the natural history of this devastating disorder.
Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient. Publishing Authors By Initials
Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient. Journal Published:
PUBLICATION TYPE: Journal Article
Journal: European journal of pediatrics
VOLUME: 167
Page Numbers: 103-5
Journal Abbreviation: Eur. J. Pediatr.
ISSN: 0340-6199
DAY: 4
MONTH: 08
YEAR: 2007
Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient. Information
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LANGUAGE: eng
NlmUniqueID: 7603873
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Grant and Affiliation Information for Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient.
AFFILIATION: Department of Pediatrics, Kansai Medical University, 10-15 Fumizonocho, Moriguchi, Osaka, 570-8506, Japan, takaya@takii.kmu.ac.jp.
Country: Germany
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MEDLINETA: Eur J Pediatr
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