Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease.

Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Research Abstract Details 

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Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Abstract Text:

T Murofushi,M Mizuno,T Hayashida,M Yamane,R Osanai,K Ito,K Kaga,

We report chronological changes of neuro-otological findings and associated neuropathological findings in 2 patients. Concerning gaze limitation, upward gaze was primarily disturbed, followed by downward gaze and abduction. Adduction tended to be preserved although convergence was disturbed at the early stage. And, upward gaze limitation was followed by loss of oculocephalic responses (OCRs). Bell's phenomenon was preserved until the late stage of the disease. Caloric nystagmus was absent at the early stage. One patient showed dissociation between nystagmus and vestibulo-collic reflex in the caloric test at the early stage of the disease. Neuropathological examination revealed gliosis in the interstitial nucleus of Cajal and the MLF as well as neuronal loss and gliosis in the oculomotor nuclei. The vestibular nuclei also showed gliosis and atrophy of nerve cells.

Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Publishing Authors By Initials

T Murofushi,M Mizuno,T Hayashida,M Yamane,R Osanai,K Ito,K Kaga,

For similar nervous system: central nervous system: brain: brain stem: rhombencephalon: metencephalon: pons: vestibular nuclei research abstracts see: nervous system: central nervous system: brain: brain stem: rhombencephalon: metencephalon: pons: vestibular nuclei research

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Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Journal Published:

PUBLICATION TYPE: Journal Article

Journal: Acta oto-laryngologica. Supplementum

VOLUME: 520 Pt 1

Page Numbers: 136-9

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ISSN: 0365-5237

DAY: 13

MONTH: 02

YEAR: 1995

Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Information

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LANGUAGE: eng

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Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease. Keywords Mesh Terms:

KEYWORDS: Vestibular Nuclei

MESH TERMS: physiopathology

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Grant and Affiliation Information for Neuro-otological and neuropathological findings in two cases with Machado-Joseph disease.

AFFILIATION: Department of Otolaryngology, Faculty of Medicine, University of Tokyo, Japan.

Country: NORWAY

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MEDLINETA: Acta Otolaryngol Suppl

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