Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections.

Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Research Abstract Details 

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Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Abstract Text:

A 10-month-old male infant had keratosis follicularis spinulosa decalvans, an X-linked dominant disorder. His cutaneous abnormalities consisted of generalized hyperkeratosis, spiny follicular papular lesions, universal alopecia, and hypoplastic nails. Ocular changes characteristic of the disease were also present. Unusual findings included deafness, failure to thrive, predisposition to bacterial infections without demonstrable immune defect, and transient hepatomegaly with abnormal liver function studies.

Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Publishing Authors By Initials

For similar bacterial infections and mycoses: infection: urinary tract infections research abstracts see: bacterial infections and mycoses: infection: urinary tract infections research

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Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Journal Published:

PUBLICATION TYPE: Research Support, U.S. Gov't,

Journal: Archives of dermatology

VOLUME: 114

Page Numbers: 761-4

Journal Abbreviation: Arch Dermatol

ISSN: 0003-987X

DAY: 17

MONTH: May

YEAR: 1978

Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Information

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LANGUAGE: eng

NlmUniqueID: 372433

Keratosis follicularis spinulosa decalvans. An infant with failure to thrive, deafness, and recurrent infections. Keywords Mesh Terms:

KEYWORDS: Urinary Tract Infections

MESH TERMS: complications

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Country: UNITED STATES

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MEDLINETA: Arch Dermatol

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