Hepatobiliary pathology in patients with cystic fibrosis.

Hepatobiliary pathology in patients with cystic fibrosis. Research Abstract Details 

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Hepatobiliary pathology in patients with cystic fibrosis. Abstract Text:

M Sinaasappel,

Overt liver disease in cystic fibrosis is a rare condition. Only 1-5% of all patients show a severe disturbance of the liver cell function or portal hypertension. In contrast, liver architecture is much more often disturbed at post mortem examination. The experience is that liver pathology increases with age which will result in rising numbers of patients in the future parallel to the increasing life expectancy of the patients. Bile plugs are commonly found in the portal tract and probably represent the essential abnormality of the liver in CF. Recently new methods have been developed for the investigation of the bile synthesis which will be helpful in the understanding of the CF defect in the liver.

Hepatobiliary pathology in patients with cystic fibrosis. Publishing Authors By Initials

M Sinaasappel,

For similar digestive system diseases: liver diseases research abstracts see: digestive system diseases: liver diseases research

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Hepatobiliary pathology in patients with cystic fibrosis. Journal Published:

PUBLICATION TYPE: Review

Journal: Acta paediatrica Scandinavica. Supplement

VOLUME: 363

Page Numbers: 45-50; discussion 50-1

Journal Abbreviation:

ISSN: 0300-8843

DAY: 20

MONTH: 02

YEAR: 1989

Hepatobiliary pathology in patients with cystic fibrosis. Information

Number of References: 18

LANGUAGE: eng

NlmUniqueID: 173166

Hepatobiliary pathology in patients with cystic fibrosis. Keywords Mesh Terms:

KEYWORDS: Liver Diseases

MESH TERMS: pathology

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Grant and Affiliation Information for Hepatobiliary pathology in patients with cystic fibrosis.

AFFILIATION: Department of Paediatrics, University Hospital/Sophia Children's Hospital, Rotterdam, The Netherlands.

Country: SWEDEN

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MEDLINETA: Acta Paediatr Scand Suppl

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