[Freeman-Sheldon's syndrome. Report of five cases]

[Freeman-Sheldon's syndrome. Report of five cases] Research Abstract Details 

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[Freeman-Sheldon's syndrome. Report of five cases] Abstract Text:

Henry Juver Vergara , Capdevila,

INTRODUCTION: Freeman-Sheldon syndrome, described in 1938, is an infrequent form of arthrogryposis. MATERIAL AND METHODS: We reviewed the files of the patients with the diagnosis of Freeman-Sheldon syndrome from 1990 to 2003, and carried out an evaluation of the clinical data, family history and malformations of extremities. RESULTS: 5 patients were included, 4 male and 1 female. Upper extremities: All patients presented adducted thumbs, 3 patients were treated with a first web release and dorsal graft with improvement of grip on larger objects. Feet: Four patients had severe bilateral rigid clubfeet, they were operated on with a posteromedial release and bilateral talectomy, satisfactory results were obtained in 4 of 6 feet according to Niki criteria. Other non orthopedic anomalies: In three patients unilateral right undescended testis; 1 right inguinal hernia. CONCLUSIONS: The patients have as common factor the whistler appearance, accompanied with mill crosses hand deformity, adducted thumbs, accompanied or not with inferior extremities deformities, intellectual capacity was normal.

[Freeman-Sheldon's syndrome. Report of five cases] Publishing Authors By Initials

HJ ,LR Capdevila,

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MEDLINE DATE: 2007 Nov-Dec

[Freeman-Sheldon's syndrome. Report of five cases] Journal Published:

PUBLICATION TYPE: Journal Article

Journal: Acta ortopédica mexicana

VOLUME: 21

Page Numbers: 338-43

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DAY: 4

MONTH: 04

YEAR: 2008

[Freeman-Sheldon's syndrome. Report of five cases] Information

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LANGUAGE: spa

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AFFILIATION: Hospital Shriners para Niños, México, D.F. Clínica de Cirugía de Mano. vergarahenry@hotmail.com

Country: Mexico

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MEDLINETA: Acta Ortop Mex

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