Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy. Abstract Text:
We present the case of a 10-year-old girl with biliary atresia in whom focal nodular hyperplasia (FNH) of the liver occurred following successful "Kasai" hepatic portoenterostomy at the age of 2 months. Her jaundice completely disappeared a few weeks after the operation. A 4-cm diameter liver tumor in segment IV was found when she was 5-years old. Needle biopsy could not establish a definitive diagnosis. Because the tumor size was not changing, she was conservatively followed by abdominal echo at an outpatient clinic. She showed progressive liver dysfunction and ongoing cirrhosis, and so at the age of 10 years, she received living donor liver transplantation at our institute. The tumor was pathologically diagnosed as a FNH. Though a FNH in biliary atresia patients is extremely rare, there are only two cases reported in the literature; it should be considered in the differential diagnosis for a hepatic nodule during a long follow-up course in patients with biliary atresia.
Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy. Publishing Authors By Initials
Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy. Journal Published:
PUBLICATION TYPE: Journal Article
Journal: Pediatric surgery international
VOLUME: 24
Page Numbers: 609-12
Journal Abbreviation: Pediatr. Surg. Int.
ISSN: 0179-0358
DAY: 15
MONTH: 12
YEAR: 2007
Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy. Information
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LANGUAGE: eng
NlmUniqueID: 8609169
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Grant and Affiliation Information for Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy.
AFFILIATION: Department of Gastrointestinal and Pediatric Surgery, Mie University Graduate School of Medicine, Edobashi 2-174, Tsu, Mie, 514-8507, Japan, yosinaga@clin.medic.mie-u.ac.jp.
Country: Germany
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MEDLINETA: Pediatr Surg Int
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