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Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases.

Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Research Abstract Details 

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  • Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Abstract Text:

    k tanakaK Tanaka,a satoA Sato,k kasugaK Kasuga,m kanazawaM Kanazawa,k yanagawaK Yanagawa,m umedaM Umeda,m tadaM Tada,m tanakaM Tanaka,m nishizawaM Nishizawa,k tanakaK Tanaka,a satoA Sato,k kasugaK Kasuga,m kanazawaM Kanazawa,k yanagawaK Yanagawa,m umedaM Umeda,m tadaM Tada,m tanakaM Tanaka,m nishizawaM Nishizawa,

    We report the four patients with chronic myositis characterized by a very slow progression with cardiomyopathy and frequently with marked respiratory muscle weakness associated with other organ-specific autoimmune diseases such as primary biliary cirrhosis. The histopathology of the muscle showed many degenerative and regenerative fibers, but inflammatory-cell infiltration were minimal. The patients showed favorable response to high-dose corticosteroid treatment. Because of these clinical features, these patients are sometimes misdiagnosed as muscular dystrophy and not treated properly. It is important to distinguish this type of treatable myositis.

    Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Publishing Authors By Initials

    k tanakaK Tanaka,a satoA Sato,k kasugaK Kasuga,m kanazawaM Kanazawa,k yanagawaK Yanagawa,m umedaM Umeda,m tadaM Tada,m tanakaM Tanaka,m nishizawaM Nishizawa,k tanakaK Tanaka,a satoA Sato,k kasugaK Kasuga,m kanazawaM Kanazawa,k yanagawaK Yanagawa,m umedaM Umeda,m tadaM Tada,m tanakaM Tanaka,m nishizawaM Nishizawa,

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    Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Journal Published:

    PUBLICATION TYPE: Journal Article

    Journal: Clinical rheumatology

    VOLUME: 26

    Page Numbers: 1917-9

    Journal Abbreviation: Clin. Rheumatol.

    ISSN: 0770-3198

    DAY: 3

    MONTH: 08

    YEAR: 2007

    Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Information

    Number of References:

    LANGUAGE: eng

    NlmUniqueID: 8211469

    Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Keywords Mesh Terms:

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    Grant and Affiliation Information for Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases.

    AFFILIATION: Department of Neurology, Brain Research Institute, Niigata University, Niigata City, Niigata, 951-8585, Japan. keiko@bri.niigata-u.ac.jp

    Country: Belgium

    Belgium Research PublicationBelgium Research Publication

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    MEDLINETA: Clin Rheumatol

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