Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases.
Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Research Abstract Details
We report the four patients with chronic myositis characterized by a very slow progression with cardiomyopathy and frequently with marked respiratory muscle weakness associated with other organ-specific autoimmune diseases such as primary biliary cirrhosis. The histopathology of the muscle showed many degenerative and regenerative fibers, but inflammatory-cell infiltration were minimal. The patients showed favorable response to high-dose corticosteroid treatment. Because of these clinical features, these patients are sometimes misdiagnosed as muscular dystrophy and not treated properly. It is important to distinguish this type of treatable myositis.
Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Publishing Authors By Initials
Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Journal Published:
PUBLICATION TYPE: Journal Article
Journal: Clinical rheumatology
VOLUME: 26
Page Numbers: 1917-9
Journal Abbreviation: Clin. Rheumatol.
ISSN: 0770-3198
DAY: 3
MONTH: 08
YEAR: 2007
Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases. Information
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LANGUAGE: eng
NlmUniqueID: 8211469
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Grant and Affiliation Information for Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases.
AFFILIATION: Department of Neurology, Brain Research Institute, Niigata University, Niigata City, Niigata, 951-8585, Japan. keiko@bri.niigata-u.ac.jp
Country: Belgium
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MEDLINETA: Clin Rheumatol
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