Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses.

Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Research Abstract Details 

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Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Abstract Text:

F S Haddad,D H Jones,A Vellodi,N Kane,M C Pitt,

Children with a mucopolysaccharidosis or mucolipidosis suffer progressive disability of the hands, particularly in relation to dysfunction of the median nerve. This is an increasing problem because bone-marrow transplantation has dramatically improved survival without apparently changing the musculoskeletal manifestations. We have reviewed 48 children with these syndromes who required carpal tunnel decompression, recording symptoms, signs, radiological, electrophysiological and operative findings, histology and upper-limb function. In these children the carpal tunnel syndrome differs from that seen in adults. Symptoms are rare but signs such as decreased sweating, pulp atrophy, thenar wasting and manual clumsiness are much more common. At operation, the flexor retinaculum was thickened and a mass of white tenosynovium engulfed the flexor tendons. Most patients had some definite nerve constriction with a thickened epineurium. Functional improvement was seen after early decompression, with some benefit from simultaneous tendon release. Regular physiotherapy helped to maintain increased hand movement. We describe our assessment protocol, the physiotherapy and operative regime and the standard functional review which helps to maximise function in the hands and upper limbs of these children.

Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Publishing Authors By Initials

FS Haddad,DH Jones,A Vellodi,N Kane,MC Pitt,

For similar investigative techniques: epidemiologic methods: epidemiologic study characteristics as topic: epidemiologic studies: case-control studies: retrospective studies research abstracts see: investigative techniques: epidemiologic methods: epidemiologic study characteristics as topic: epidemiologic studies: case-control studies: retrospective studies research

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Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Journal Published:

PUBLICATION TYPE: Journal Article

Journal: The Journal of bone and joint surgery. British vol

VOLUME: 79

Page Numbers: 576-82

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ISSN: 0301-620X

DAY: 14

MONTH: Jul

YEAR: 1997

Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Information

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LANGUAGE: eng

NlmUniqueID: 375355

Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses. Keywords Mesh Terms:

KEYWORDS: Retrospective Studies

MESH TERMS: pathology

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Grant and Affiliation Information for Carpal tunnel syndrome in the mucopolysaccharidoses and mucolipidoses.

AFFILIATION: Hospital for Sick Children, London, England.

Country: ENGLAND

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MEDLINETA: J Bone Joint Surg Br

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